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Anti-TFP1/HADHA Rabbit Polyclonal Antibody

Dodavatel: BioVision
BIOV3721-100EA 8460 CZK
BIOV3721-100
Anti-TFP1/HADHA Rabbit Polyclonal Antibody
Protilátky
Mitochondrial Trifunctional Protein (TFP) is a multienzyme complex of the beta-oxidation cycle. TFP deficiency is a clinically heterogeneous disorder with phenotypes of different severity. The spectrum of diseases range from severe neonatal/infantile cardiomyopathy and early death to mild chronic progressive sensorimotor poly-neuropathy with episodic rhabdomyolysis. Human TFP is an octomer composed of four alpha-subunits and four beta-subunits. Mutations in either subunits may result in general TFP deficiency with reduced activity of all enzymes.

Recommended Dilutions: Western Blot: 0.5-4 µg/ml

Type: Primary
Antigen: TFP1/HADHA
Clonality: Polyclonal
Clone:
Conjugation: Unconjugated
Epitope:
Host: Rabbit
Isotype: IgG
Reactivity: Human, Mouse, Rat
Objednat

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